Celine Dion revealed on Thursday that have been diagnosed with stiff person syndrome, a rare and incurable neurological disease that can cause muscle spasms.
In a moving video posted on her Instagram account in English and French, the Canadian singer announces that her state of health forces him to postpone and cancel a series of concerts”, as reported by ‘People’.
What is this disease?
the stiff person syndrome (Either ‘stiff man’ in English) is characterized by a table of muscle stiffness and spasms trunk and arm and leg muscles, which are often produced by increased sensitivity to noise, touch, and response to startle. People with the syndrome may also assume abnormal postures. Disease It affects women more than men.
We think it’s a disease autoimmune in which the immune system attacks its own central nervous system (brain and spinal cord). It is frequently associated with other autoimmune diseases such as diabetes, thyroiditis, vitiligo and pernicious anemia. In fact, it often appears in people with type 1 diabetes, certain autoimmune diseases, or certain types of cancer.
What happens to the sick?
The muscles of people who suffer from this disease they gradually become more rigid and increase in size; the process begins in the trunk and abdomen and eventually affects muscles throughout the body.
Doctors suspect stiff-person syndrome based on the symptom, but they use electromyography and the blood test to help confirm the diagnosis.
Treatment focuses on relieve symptoms (incurable) and may consist of the administration of diazepam (a sedative), baclofen (a muscle relaxant) and corticosteroids and sometimes rituximab or in addition to plasmapheresis (plasma exchange).